AL型心肌淀粉样变的诊疗进展

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Abstract The mechanism of myocardial amyloidosis is the deposition of insoluble amyloid in myocardial tissue，a disease that causes cardiac dysfunction such as impaired myocardial electrical activity, cardiac hypertrophy, increased myocardial stiffness, and decreased diastolic function. Primary amyloidosis and amyloidosis associated with plasma cell disease are all immunoglobulin light chains, so they are collectively referred to as AL-type amyloidosis. Early symptoms of myocardial amyloidosis are not obvious, but as the disease progresses, symptoms of myocardial diastolic function may appear, which often indicates poor prognosis. Among them, AL-type myocardial amyloidosis is more common than other types, so this article focuses on the early clinical manifestations, staging and prognosis ,treatment of AL-type myocardial amyloidosis.

Key words： AL type myocardial amyloidosis Staging and prognosis Early diagnosis Treatment

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	Zhu Jialiang1
	2 Li Guohua2

Cite this article:

Zhu Jialiang1,2 Li Guohua2. Progress in diagnosis and treatment of AL-type myocardial amyloidosis[J]. 中国医药导报, 2019, 16(12): 50-53,57.

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http://www.yiyaodaobao.com.cn/EN/ OR http://www.yiyaodaobao.com.cn/EN/Y2019/V16/I12/50

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