少见型韧带样纤维瘤病的鉴别诊断及影像学表现特征分析

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Abstract Objective To explore the imaging manifestation of rare desmoid-type fibromatosis (DF), in order to further improve the diagnostic accuracy of the disease. Methods The clinical and imaging findings of 8 patients with DF confirmed by surgery and pathology from July 2015 to October 2017 in the First Affiliated Hospital of University of Science and Technology of China Anhui Provincial Hospital were retrospectively analyzed. The location and boundary of the lesion were analyzed, and the chayacteristics and differential diagnosis of computed tomography (CT) and magnetic resonance （MR） imaging were analyzed. Results In the 8 patients, 5 cases were abdominal wall type, and 3 cases were intra-abdominal type. Seven cases had a history of abdominal surgery in the 8 cases. The abdominal wall showed infiltrative growth, and it was not clear with the rectus abdominals muscle. The spindle shape was the most common form, and the growth axis was parallel to the muscle fiber. The intra-abdominal type was mainly inflated growth, with varied morphology and clear boundary. CT scan: the lesions showed soft tissue density, low density area could be seen, with rare calcification and hemorrhage, boundary was less clear. MR scan: T1WI showed equal or slightly low signal, T2WI showed a slightly uneven high signal, low signal area could be seen; enhanced scanning showed progressive enhancement. Conclusion Abdominal wall type and intra-abdominal type desmoid fibromatosis have certain characteristics in clinical data, CT and MR imaging, which is of great value for the correct diagnosis of this disease.

Key words： Abdominal wall type desmoid fibromatosis Intra-abdominal type desmoid fibromatosis；Computed tomography Magnetic resonance Diagnosis

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	WANG Minrui DENG Kexue

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WANG Minrui DENG Kexue. Analysis on the differential diagnosis and imaging features of rare desmoid-type fibromatosis[J]. 中国医药导报, 2018, 15(34): 135-139.

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http://www.yiyaodaobao.com.cn/EN/ OR http://www.yiyaodaobao.com.cn/EN/Y2018/V15/I34/135

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