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| Pulmonary artery intimal sarcoma as a rare cause of pulmonary hypertension: a case report |
| CAI Bin1 AI Juan1 LI Xiangyu1 ZHENG Yuan2 LING Qiong1 YANG Manmei3▲ |
1.Department of Anesthesiology, University City Hospital, Guangdong Provincial Hospital of Chinese Medicine, Guangdong Province, Guangzhou 515000, China;
2.the Second Department of Cardiac Surgery, University City Hospital, Guangdong Provincial Hospital of Chinese Medicine, Guangdong Province, Guangzhou 515000, China;
3.Ward Two of ICU, Chenzhou First People’s Hospital, Hunan Province, Chenzhou 423000, China
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Abstract Pulmonary artery intimal sarcoma (PAIS) is a rare disease with a high misdiagnosis rate. Because the onset is easy to be confused with other cardiovascular diseases, once misdiagnosed or missed diagnosis, resulting in further development of the disease, miss the best treatment opportunity. In order to improve the level of clinical diagnosis and treatment of this disease and make correct diagnosis and treatment plan, a case of PAIS was reported and analyzed in Guangdong Provincial Hospital of Chinese Medicine. The first symptoms of the patient were progressive chest tightness and asthma. The patient was considered to be PAIS through preoperative physical examination, imaging examination, and combined with previous medical history. The pulmonary artery tumor was excised under cardiopulmonary bypass, during which gray and white masses were found to invade the whole layer of blood vessels along the main pulmonary artery. The tumor was completely resected, and PAIS was confirmed by postoperative pathological examination. The patient died of multiple organ failure one month after surgery. Through retrospective analysis of domestic and foreign literature, most of them believe that once PAIS is diagnosed, surgery and concurrent chemorotherapy should be actively treated; at the same time, literature review was carried out on the symptoms, clinical manifestations, imaging features of the disease to improve the understanding of the disease, so as to reduce misdiagnosis or missed diagnosis.
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