Abstract：ALS patients always occure respiratory muscle weakness, acute respiratory failure and respiratory muscle paralysis caused by pulmonary infection are the most common cause of death in ALS patients. It is very important for ALS patients to be evaluated regularly and timely hospitalized assessment. This article reviews the respiratory support process of an ALS patients with acute type Ⅱ respiratory failure. After the patient admitted to hospital, the blood gas analysis suggested that type Ⅱ respiratory failure, according to the patient's breathing state, blood gas analysis results and personal wishes, he was treated with non-invasive ventilation, tracheal intubation assisted ventilation and tracheotomy after transferred into the neurological ICU by sequence, and given adequate nutritional support, Antibiotic treatment of infection, expectorant and other symptomatic treatment care at the same time. After the systematic treatment, the patient's condition became stable and transferred to long-term carefacility. Generally, in patients with auxiliary ventilation indications, choosing the appropriate respiratory support measures and regular adjustments according to the disease and personal wishes can help improve the patients' respiratory function.
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2018, Vol. 15 
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