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| A case of POEMS syndrome misdiagnosed as chronic inflammatory demyelinating polyneuropathy |
| ZHANG Na CHEN Zhigang LI Nannan |
| Ward One, Department of Neurology, Dongfang Hospital Attached to Beijing University of Traditional Chinese Medicine, Beijing 100078, China |
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Abstract The clinical data of a case of retroperitoneal schwannoma in the Dongfang Hospital Attached to Beijing University of Traditional Chinese Medicine in 2018 were analyzed retrospectively in order to investigate the diagnosis and treatment of POEMS syndrome. Multiple peripheral neuropathy is not only the main clinical manifestation of POEMS syndrome patients, but also the first symptom. Almost all patients with this disease have the protein cell separation phenomenonin in the cerebrospinal fluid, which is easy to be misdiagnosed with chronic inflammatory demyelinating polyneuropathy (CIDP). Early treatment is beneficial to reduce the degree of disease damage and increase the survival rate, so early diagnosis is very important. This patient was misdiagnosed as CIDP for two and a half years. During this period, the patient developed multiple system symptoms, and went to many departments of many hospitals for treatment. While, the patient was not diagnosed correctly all the time. The patient was suffering physically and mentally, which cost a lot of human, material and financial resources. In this study, the case report combined with literature review can help guide clinicians to correctly diagnose patients with POEMS syndrome as soon as possible, so that patients can benefit the most.
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